Navigating Cystic Fibrosis: The Integral Role of Pediatric Nurses in Managing Complex Needs

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[...] Moreover, nurses coordinate care across multidisciplinary teams, advocate for specialized services, and ensure continuity of care across settings, prioritizing smoking cessation, immunizations, infection prevention, and CF management to empower patients and families in shared decision-making. References Brackeen, M. (2021, February 2). How CF has affected our family dynamic. Cystic- Fibrosis.com. https://cystic-fibrosis.com/caregiver/affect-family-dynamic Centers for Disease Control and Prevention. (2022, November 30). Cystic fibrosis. https://www.cdc.gov/genomics/disease/cystic_fibrosis.htm Cox, A., & Pritchard, C. (2020). Hearing the Voice of a Shadow Child: Healthy Siblings Experience of Cystic Fibrosis and Other Life-Threatening Conditions. Journal of Patient Experience, 878-881. https://doi.org/10.1177/2374373520948652 Girón Moreno, R. M., García-Clemente, M., Diab-Cáceres, L., Martínez-Vergara, A., Martínez- García, M. Á., & Gómez-Punter, R. [...]

[...] In addition, modern cystic fibrosis treatment modulates CFTR. New medications directly target the faulty CFTR protein to boost cellular function and reduce thick mucus and respiratory and gastrointestinal issues (Girón Moreno et al., 2021). Besides, other drugs often accompany CFTR modulators. Lung infections caused by sticky mucus bacteria are treated with antibiotics-Mucolytics thin mucus, making it more straightforward to remove and minimizing infection. Assessment of illness progression and treatment efficacy requires regular clinical exams. Blood, imaging, and lung function testing evaluate patients and alter treatment. [...]

[...] The operation increases lung function, decreases infections, and improves breathing, offering patients a new life. Lifelong immunosuppression is needed to prevent lung transplant rejection. The transplant recipient must be healthy for surgery and recovery. Post-Surgical Considerations- Extra attention is needed to avoid lung transplant problems. Anti-organ rejection immunosuppressants increase infection risk. After surgery, lung specialists, transplant surgeons, and other doctors must see patients regularly (Cox & Pritchard, 2020). Therefore, post-surgical considerations examine lung function, rejection, and adverse effects of drugs. [...]

[...] Navigating Cystic Fibrosis: The Integral Role of Pediatric Nurses in Managing Complex Needs Cystic Fibrosis is a dangerous inherited condition that damages children's and young adults' lungs and digestion. The disease is characterized by thick, sticky mucus that complicates respiratory and gastrointestinal issues. As a result, family members suffer chronic clinical problems and emotional and physical stress. Chronic illness patients undergo medical, surgical, and holistic therapy to improve their health (Mayo Clinic, 2021). Therefore, according to this study, pediatric nurses must meet CF patients' complex demands with improved clinical procedures and compassionate, patient-centered care. [...]

[...] According to the Centers for Disease Control and Prevention. (2022), these networks provide daily psychological and practical disease management support. CF patients can exchange stories, thoughts, and techniques in support groups. Sreenivasulu et al. (2023) highlight that these organizations promote understanding and lessen family separation and misery. At seminars, healthcare practitioners teach families about new treatments and research to help them manage the disease Local non-profits provide counselling, financial aid, medical equipment, and food. The provided resources and healthcare practitioners handle families holistically. [...]